ALDH6A1 antibody
Cat.#: S1054
Rabbit Polyclonal Antibody
Clone ID: polyclonal
Swiss Prot: Q02252
Mol Weight: 57.85kDa
Size: 100ug

Description
This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. [provided by RefSeq]

Recommended Applications
WB

Applications and Recommended Dilution Factors
WB: 1:500-1:3000

Species Reactivity
Human

Other species have not been tested

Products Data

 
Sample(30 ug whole cell lysate)
A:Hep G2
7.5% SDS PAGE
diluted at 1:500

Specificity
Recombinant protein fragment contain a sequence corresponding to a region within amino acids 219 and 526 of Human ALDH6A1

Storage Condition and Buffer
0.1M Tris, 0.1M Glycine, 10% Glycerol (pH7.0). 0.01% Thimerosal was added as a preservative. Keep as concentrated solution. Aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles. Purified by antigen-affinity chromatography.

Alternative Names
ALDH6A1 antibody, MGC40271 antibody, MMSADHA antibody, MMSDH antibody, Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial antibody, Aldehyde dehydrogenase family 6 member A1 antibody