ALAS-E antibody
Cat.#: S1738
Rabbit Polyclonal Antibody
Clone ID: polyclonal
Swiss Prot: P22557
Mol Weight: 64.64kDa
Size: 100ug

Description
The product of this gene specifies an erythroid-specific mitochondrially located enzyme. The encoded protein catalyzes the first step in the heme biosynthetic pathway. Defects in this gene cause X-linked pyridoxine-responsive sideroblastic anemia. Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq]

Recommended Applications
WB

Applications and Recommended Dilution Factors
WB: 1:500-1:3000

Species Reactivity
Human

Other species have not been tested

Products Data

Sample(30ug of whole cell lysate)
A: A431
B: H1299
C: HeLa S3
D: Hep G2
E: MOLT4
7.5% SDS PAGE
diluted at 1:1000

Specificity
Recombinant protein fragment contain a sequence corresponding to a region within amino acids 211 and 567 of Human ALAS2

Storage Condition and Buffer
0.1M Tris, 0.1M Glycine, 10% Glycerol (pH7.0). 0.01% Thimerosal was added as a preservative. Keep as concentrated solution. Aliquot and store at -20ºC or below. Avoid multiple freeze-thaw cycles. Purified by antigen-affinity chromatography.

Alternative Names
ALAS2 antibody, ALAS-E antibody, ALASE antibody, ANH1 antibody, ASB antibody, FLJ93603 antibody, XLDPP antibody, XLSA antibody, 5-aminolevulinate synthase, erythroid-specific, mitochondrial antibody, 5-aminolevulinic acid synthase 2 antibody, Delta-ALA synthase 2 antibody, Delta-aminolevulinate synthase 2 antibody